Intestinal obstruction mimicking intra-abdominal hemorrhage in a teenager with familial thrombocytopenia: a case report
Keywords:
Intestinal obstruction, intra-abdominal hemorrhage, teenager, familial thrombocytopenia
Abstract
Inherited bleeding disorders are a heterogeneousgroup of disease that is complicated by
hemorrhagic episodes, spontaneous, and post-
traumatic. Included in this category of conditions
are Familial Thrombocytopenias (FT). FT are a
heterogeneous group of inherited disorders that vary
in severity with regard to the degree of reduction in
platelet counts and in expression of bleeding
manifestations. As in acquired thrombocytopenias, FT
patients are at risk for hemorrhagic complications.
Rarely, patients with inherited non-thrombocytopenia
bleeding disorders can develop complications of acute
abdomen 1,2 which present as intraabdominal
hemorrhage. We report a case of intestinal obstruction
mimicking an uncomplicated intraabdominal
hemorrhage in a teenager with FT.
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tra-abdominal hemorrhage due to a ruptured corpus
luteum cyst in a girl with congenital afibrinogenemia.
Eur J Ped 2001;160:196.
3. Maltz GS, Siegel JS, Carson JL. Hematologic manage-
ment of gastrointestinal bleeding. Gastroenterol. Clin
North Am 2000;29:169-87.
4. Cohn, J. Thrombocytopenia in childhood: an evalua-
tion of 433 patients.Scand J Hematol 1976;16:226-40.
6. Chiu CH, Tsai JR, Ou JT, Lin Ty. Typhoid fever in chil-
dren: a fourteen-year experience. Acta Pediatr Taiwan
2000;41:28-32.
7. Sunarto, Sutaryo. Thrombocytopenia in dengue hem-
orrhagic fever. Pediatr Indones 1992;32:75-83.
8. College of American Pathologists. Practice parameter
for the use of fresh-frozen plasma, cryoprecipitate and
platelets. JAMA 1994;271:777-81.
9. Rodeghiero F, Castaman G, Manucci PM. Prospec-
tive multicenter study on subcutaneous concentrated
desmopressin for home treatment of patients with von
Willebrand disease and mild or moderate hemophilia
A. Thromb Haemost 1996;76:692-6.
10. Everlien M, Knoch K, Farah I, Greve H. Coronary by-
pass surgery in May-Hegglin anomaly. Deutsche
medizinische Wochenschrift 2001;126:47-9.
12. Martinez-Murillo C, Quintana-Gonzalez S, Ambriz-
Fernandez R, Arzate-Hernandez G, Guitierrez-
Romero M, Gaminio - Gomez E. Utility of
desmopressin in 4 cases of thrombocytpathies associ-
ated with giant platelets. Rev Invest Clin
1997;49:281-6.
13. Kosch A, Kehrel B, Nowak-Gottl U, Haberle J, Jurgens
H. Thrombocytic alpha-delta storage pool disease:
shortening of bleeding time after infusion of l-
desamino-8-D-arginine vasopressin. Klin Padiatr
1999;211:198-200.
14. Stubbs M, Lloyd J. A protocol for the dental manage-
ment of von Willebrand’s disease, hemophilia A and
hemophilia B. Aust Dent J 2001;46:37-40.
15. Rakocz M, Lavie G, Martinowitz U. Glanzmann’s
thrombasthenia: the use of autologous fibrin glue
in tooth extractions. ASDC J Dent Child
1995;62:129-31.
Published
2016-10-10
How to Cite
1.
Sutaryo S, Ali K, Widodo U, Agustriyani N, Moeljono E, Belletrutti M. Intestinal obstruction mimicking intra-abdominal hemorrhage in a teenager with familial thrombocytopenia: a case report. PI [Internet]. 10Oct.2016 [cited 23Dec.2024];43(3):106-. Available from: https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/671
Section
Case Report
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Received 2016-09-23
Accepted 2016-09-23
Published 2016-10-10
Accepted 2016-09-23
Published 2016-10-10
