Prune-belly syndrome

Main Article Content

Yenny Yenny
Kusuma P. A
Damanik M. P.


Prune-belly syndrome, also known as Eagle-Barret
syndrome, is a congenital anomaly comprising
three clinical findings: deficient abdominal
musculature, urinary tract anomalies, and
bilateral cryptorchidism. Other clinical findings involving
respiratory, skeletal, digestion and cardiovascular system
may also accompany the syndrome. The incidence is
approximately 1 : 30,000 to 40,000 live births and 95%
of cases occur in boys. Pulmonary hypoplasia and kidney
failure are important prognostic factors that contribute
to 60% of mortality rate. Treatment includes surgical
correction of the abdominal wall and urinary tract,
orchidopexy and other supportive managements.l-4 We
report 4 cases on typical Prune-belly syndrome, together
with other clinical variants.

Article Details

How to Cite
Yenny Y, P. A K, M. P. D. Prune-belly syndrome. PI [Internet]. 31Oct.2009 [cited 27Nov.2020];49(5):304-. Available from:
Case Report
Author Biographies

Yenny Yenny

Department of Child Health, Medical School, Gadjah Mada University, Dr. Sardjito Hospital, Yogyakarta, Indonesia.

Kusuma P. A

Department of Child Health, Medical School, Gadjah Mada University, Dr. Sardjito Hospital, Yogyakarta, Indonesia.

Damanik M. P.

Department of Child Health, Medical School, Gadjah Mada University, Dr. Sardjito Hospital, Yogyakarta, Indonesia.
Received 2016-09-11
Accepted 2016-09-11
Published 2009-10-31


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