Circumcision in boys with mild Hemophilia A â€“ the Yogyakarta experience

Pudjo Hagung Widjajanto; Ridwan Tjandra Sugiarto; Sutaryo Sutaryo; Kaiser Ali

doi:10.14238/pi47.2.2007.71-3

Pudjo Hagung Widjajanto
Ridwan Tjandra Sugiarto
Sutaryo Sutaryo
Kaiser Ali

DOI: https://doi.org/10.14238/pi47.2.2007.71-3

Keywords: circumcision, mild hemophilia A, electrocautery, laser surgery

Abstract

Background In boys with hemophilia, there is a risk of
hemorrhage resulting from circumcision. There has been no
standardised management in Indonesia. We report our experience
with 4 hemophiliac boys who underwent circumcision at Dr.
Sardjito General Hospital, Yogyakarta, in south-central Java.
Objective To develop a safe, practical and accessible method to
prevent bleeding in boys with hemophilia undergoing circumcision
in Indonesia.
Methods Written informed consent was obtained from parents
requesting the procedure. All boys had mild Hemophilia A (VIII:
C level >7.8 U/ml) diagnosed at a median age of 4.4 years (range
0.75â€“9 years). Median age at time of circumcision was 7.5 years
(range 0.8â€“12 years).
Results There were no intraoperative or post-circumcision
bleeding problem encountered in any of the patients, who were
discharged from hospital three days post-surgery. On follow up
eight days and 12 days post-circumcision, they remained free of
complications.
Conclusion Circumcision can be safely performed in boys with
mild Hemophilia A following adequate pre-operative planning
and prophylactic therapy. A standardised protocol for the
Yogyakarta Bleeding Disorders Program. evolving from this
experience, is being planned.

Author Biographies

Pudjo Hagung Widjajanto

Department of Child Health, Medical School, Gadjah Mada University, Yogyakarta, Indonesia.

Ridwan Tjandra Sugiarto

Department of Child Health, Medical School, Gadjah Mada University, Yogyakarta, Indonesia.

Sutaryo Sutaryo

Department of Child Health, Medical School, Gadjah Mada University, Yogyakarta, Indonesia.

Kaiser Ali

Department of Child Health, Medical School, University of Saskatchewan, Canada.

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