Hand-Schuller-Christian disease

  • Sjabaroeddin Loebis Department of Child Health, University of Sumatera Utara Medical School, Medan, North Sumatera
  • Bistok Saing Department of Child Health, University of Sumatera Utara Medical School, Medan, North Sumatera
  • Helena Siregar Department of Child Health, University of Sumatera Utara Medical School, Medan, North Sumatera
  • M. Najib Loebis Department of Histopatology, University of Sumatera Utara Medical School, Medan, North Sumatera
DOI: https://doi.org/10.14238/pi21.9-10.1981.205-14
Keywords: Hand-Schuller-Christian disease, histocytosis X

Abstract

A 14-month-old girl was admitted with signs of paleness, weakness and swelling of the lymphnodes in the neck and inguinal. Histopatological examination of the lymphnodes showed histiocytosis X. X-photo of the skull and pelvic bones revealed several osteolysis.

Based upon clinical manifestations and histopathological examination this diseases was diagnosed as the rare disease Hand-Schüller-Christian disease.

References

1. AVERY, M.E.; Me AFEE, I.G. and GUILD, H.G.: The Course and prognosis of reticuloendotheliosis (eosinophilic granuloma, Schuller-Christian disease and LeHerer-Siwe disease). Amer. J. Med. 22 : 636 (1957).
2. BEIER F.R.; THATCHER, L.G. and LAHEY, M.E.: Treatment of reticuloendothelioisis with vinblastine sulfate. Pediatr. 63 : 1087 (1963).
3. BLAHD, W.H.; LEVY, M.s. and BASSETT, S.H.: A case of Hand-Schuller Christian syndrome treated with cortisone. Ann. intern. Med. 35 : 927 (1951).
4. CHEYNE. C.: Histiocytosis X. Journal of bone and Joint Surgery 538: 366 – 382 (1971).
5. LICHTENSTEIN, L : Histiocytosis X. Integration of eosinophilic granuloma of bone "Letterer-Siwe disease" as related manifestations of a single nosologic entity. Arch. Pothol. 56 : 84 (1973).
6. MERMANN, A.C. and DARGEON, H.W.: The management of certain non lipid reticuloendotheliosis. Cancer. 8: 112 (1955).
7. OBERMAN, H.A. : Idiopathic histiocytosis X. A clinicopathologic sludy or 40 cases and review of the literature On eosinophilic granuloma of bone. Hand-Schüller-Christian disease and Letterer. Siwe disease. Pediatr. 28: 307 (1961).
8. SIEGEL, J.S. and COLTMAN, C.A. : Histiocytosis X. Response to vinblastine sulfate. J. Amer. Ass. 1971 123 (1966).
9. STARLING, K.E., DONALDSON, M.H., HAGGARD, M.E.; VIETTI, T.I. and SUTOW, W.W. : Therapy of histiocytosis X with vincristine, vinblastine and cyclophosphamide. Amer. J. Dis. Child. 123 : 105 (1972).
10. SIMS. D.O. : Histiocytosis X, Arch. Dis. Child. 52: 433-440 (1977).
11. WIDAGDO; SADELI, R., WAHIDIYAT, I.: Hand-Schüller-Christian disease (Case Report). Pediatr. Indon. 14: 218-223 (1974).
Published
1981-10-30
How to Cite
1.
Loebis S, Saing B, Siregar H, Loebis M. Hand-Schuller-Christian disease. PI [Internet]. 30Oct.1981 [cited 30Apr.2024];21(9-10):205-4. Available from: https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/1198
Issue
Vol 21 No 9-10 (1981): September - October 1981
Section
Case Report

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Received 2017-01-26
Accepted 2017-01-26
Published 1981-10-30