Renal manifestations in tuberous sclerosis patients: two case reports

Main Article Content

Oke Rina Ramayani
Rosmayanti Rosmayanti
Rafita Ramayati
Rusdidjas Rusdidjas


Tuberous sclerosis (TS) is a neurocutaneous disorder, characterized by
mental retardation, epilepsy, and facial
angiofibromas. The incidence has been
estimated to be 1 case per 6000 live births.
Although rare, this disorder is a cause of mental
retardation with severe epilepsy.1 Scientists have
found manifestations of this disorder not only in
brain and skin, but also in the eyes, heart, lungs, and
kidneys, so it has been renamed tuberous sclerosis
complex (TSC).

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How to Cite
Ramayani O, Rosmayanti R, Ramayati R, Rusdidjas R. Renal manifestations in tuberous sclerosis patients: two case reports. PI [Internet]. 28Feb.2013 [cited 8Jul.2020];53(1):56-. Available from:
Received 2016-08-18
Accepted 2016-08-18
Published 2013-02-28


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