Successful treatment of Budd-Chiari Syndrome with Rivaroxaban in a six week old Bangladeshi infant

  • Mukesh Khadga Doctor
  • Ferdous Ara Begum Doctor
  • Mohammad Wahiduzzaman Mazumder Doctor
  • Mohammad Benzamin Doctor
  • Nazmul Ahamed Rony Doctor
  • Abu Zafor Mohammad Raihanur Rahman Doctor
  • Ayesha Siddiqua Doctor
  • Nazmul Hassan Doctor
  • Abu Sayed Mohammad Bazlul Karim Doctor
Keywords: abdominal distension; Budd-Chiari syndrome; children; hepatic venous outflow obstruction

Abstract

Budd-Chiari syndrome (BCS) is the clinical spectrum presenting with hepatic venous outflow obstruction from the hepatic veins to the junction of the inferior vena cava (IVC) and the right atrium. This syndrome is rare in infants and children, which leads to misdiagnoses or delayed diagnoses. Clinical presentations may be non-specific. A high index of suspicion and imaging findings may help in early diagnosis of this condition. We report a rare case of BCS in a 6-week-old male infant who presented with jaundice and gradual abdominal distension. He was successfully treated with rivaroxaban.

Author Biographies

Ferdous Ara Begum, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Mohammad Wahiduzzaman Mazumder, Doctor

Associate Professor, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Mohammad Benzamin, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Nazmul Ahamed Rony, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Abu Zafor Mohammad Raihanur Rahman, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Ayesha Siddiqua, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Nazmul Hassan, Doctor

Resident, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

Abu Sayed Mohammad Bazlul Karim, Doctor

Professor, Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh.

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Published
2022-03-04
How to Cite
1.
Khadga M, Begum F, Mazumder M, Benzamin M, Rony N, Rahman AZM, Siddiqua A, Hassan N, Karim ASM. Successful treatment of Budd-Chiari Syndrome with Rivaroxaban in a six week old Bangladeshi infant. PI [Internet]. 4Mar.2022 [cited 24Nov.2024];62(2):138-2. Available from: https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/2434
Section
Case Report
Received 2020-06-06
Accepted 2022-03-04
Published 2022-03-04