Right Isomerism

  • Ismet N. Oesman Department of Child Health, Universitas Indonesia Medical School/Dr. Cipto Mangunkusumo Hospital, Jakarta
  • Hindra Irawan S. Department of Child Health, Universitas Indonesia Medical School/Dr. Cipto Mangunkusumo Hospital, Jakarta
  • Bambang Mardiono Department of Child Health, Universitas Indonesia Medical School/Dr. Cipto Mangunkusumo Hospital, Jakarta
  • Sudigdo Sastroasmoro Department of Child Health, Universitas Indonesia Medical School/Dr. Cipto Mangunkusumo Hospital, Jakarta
DOI: https://doi.org/10.14238/pi32.7-8.1992.226-34
Keywords: right isomerism; heart malformation; vomit; duodenostomy

Abstract

A rare case of complex heart malformatrion with right isomerism in a full-term baby boy which was the first case published in Indonesia is reported. The patient was initially managed as a healthy baby, but on the 20th hours after delivery he repeatedly vomitted, and from the rontgenographic finding diagnosis at that time was duodenal atresia. During the duodenostomy operation the surgeon noticed that the spleen was absent. Cyanosis appeared after operation. Techocardiography and electrocardiography was done immediately, which showed complex cyanotic congenital heart disease. Diagnosis complex cyanotic congenital heart disease with right isomerism then was suspected. Unfortunately the baby died on the 12th day of admission. 1be cause of death was sepsis and anoxia because of complex cyanotic congenital heart disease. Autopsy findings confirmed the diagnosis of right isomerism (bilateral trilobes lung, bilateral right atrial appendages).

References

14. Satomi G, Takao A. Systemic diagnostic method of two dimensional echocardiography in congenital heart disease. Heart and vessels 1985 ; 1 : 101-13.
15. Di-Donato R, Di-Carlo D, Squitieri C. et al. Palliation of cardiac malformations associated with right isomerism (asplenia syndrome) in infancy. Ann Thorac Surg 1987; 44: 5 - 39.
Published
2019-01-30
How to Cite
1.
Oesman I, S. H, Mardiono B, Sastroasmoro S. Right Isomerism. PI [Internet]. 30Jan.2019 [cited 25Apr.2024];32(7-8):226-4. Available from: https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/2119
Issue
Vol 32 No 7-8 (1992): July - August 1992
Section
Case Report

Copyright (c) 2019 Ismet N. Oesman, Hindra Irawan S., Bambang Mardiono, Sudigdo Sastroasmoro

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Received 2019-01-30
Published 2019-01-30