A Case of Thalassemia-Hb S Disease in Jakarta

  • Iskandar Wahidijat Department of Child Health, Medical School, University of Indonesia, Jakarta
  • A. H. Markum Department of Child Health, Medical School, University of Indonesia, Jakarta
  • S. Moeslichan Department of Child Health, Medical School, University of Indonesia, Jakarta
DOI: https://doi.org/10.14238/pi14.7-8.1974.128-31
Keywords: thalassemia-Hb S disease, Jakarta

Abstract

The first Hb S (Hb S trait) in

Indonesia, was found by Lie-Injo

Luan Eng (1956) in Jakarta. As

far as we know the case presented

in this paper, is the first patient with

thalassemia-Hb S disease ever found

in the Indonesian literature.

References

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LIE-INJO LUAN ENG: Penyelidikan hemoglobin patologik di Indonesia (1956). Tesis.

LIE-INJO LUAN ENG: Sickle-cell gene in Indonesia. Nature 179 : 381 (1957).

MOTULSKY, A.G.; PAUL, M.H. and DURRUM, E.L.: Paper electrophoresis of abnormal hemoglobins and its clinical applications, a simple semiquantitative method for the study of the hereditary hemoglobinopathies. Blood 9 : 897 (1954).

PEARSON, H.A.: Hemoglobin S-Thalassemia syndrome in Negro children. Ann. N.Y. Acad. Sci. 165 : 83 (1969).

SILVESTRONI, E. and BIANCO. I.: Microdrepanocito - anemia in un soggetto di razza bianca. Boll. Atti. Acad. Mod. Roma 70 : 347 (1944). Cited from: PEARSON, H.A.: Hemoglobin S-Thalassemia syndrome in Negro children. Ann. N.Y. Acad. Sci. 165 : 83 (1969).

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WENT, L.N. and MAC IVER, J.E.: Sickle-cell anaemia in adults and its differentiation from sickle-cell thalassemia. Lancet 2 : 824 (1958).

ZUELZER, W.W. : Clinical and haematological aspects of the various haemoglobin syndrome. In abnormal haemoglobins. Ed. JONXIS, J.H.P. and DELAFRESNAJE, J.F., p. 100. Blacwell Scientific Publications. Oxford.
Published
2017-06-09
How to Cite
1.
Wahidijat I, Markum A, Moeslichan S. A Case of Thalassemia-Hb S Disease in Jakarta. PI [Internet]. 9Jun.2017 [cited 27Apr.2024];14(7-8):128-1. Available from: https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/1497
Issue
Vol 14 No 7-8 (1974): July - August 1974
Section
Articles

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Received 2017-06-08
Accepted 2017-06-08
Published 2017-06-09